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HIRURŠKI ASPEKT LEČENJA BRONHIEKTAZIJA KOD KARTAGENEROVOG SINDROMA

SURGICAL ASPECTS OF THE TREATMENT OF BRONCHIECTASIS IN KARTAGENER'S SYNDROME

Authors

 

Nebojša Marić1, Dejan Stojković1, Vlado Cvijanović1, Aleksandar Ristanović1, Nataša Vešović1, Vanja Kostovski1, Bojana Miranović1, Milena Pandrc2, Ljubinko Đenić1

1 Klinika za grudnu hirurgiju, Vojnomedicinska akademija, Beograd, Srbija
2 Odeljenje stacionarnog lečenja Vojne akademije, Beograd, Srbija

 

• The paper was received on 10.11.2015. / Accepted on 14.12.2015.

 

Abstract

 

Introduction. Kartagener ’s syndrome is a hereditary autosome-recesive disease which is characterized by the structual and general imotile cilia of spermatozoids, bronchial epitel and situs inversus (1) .The main aim of this artical is to point out the importance of the surgical treatment in the prevention of the complications of the Kartagener ’s syndrome.
Case report. A male patient, in the age of  37 with Kartagener ’s syndrome and  thorax anomaly – pectus carinatum  is diagnosed by multislice computerized tomography
(MSCT) , that emphased  an inversion of thoracal and abdominal organs. The spermogram is pointed out the  imotile spermatozoids beacuse of a ciliary dyskinesia, but not infertility which is very frequent in this syndrome(2) . The disorders in ventilation of the obstructive-restrictive type and of the arterial gase were presented. The left posterior lobectomy and a lower lobectomy were done.
Conclusion. Elective surgical treatment of the Kartagener’s syndrome decreases a repetition of respiratory infections.

 

 

References

 

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PDF Marić N. • MD-Medical Data 2015;7(4): 319-321

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