md-medicaldata

Authors

 

Nebojša Marić¹, Dejan Stojković¹, Vlado Cvijanović¹, Aleksandar Ristanović¹, Nataša Vešović¹, Vanja Kostovski¹, Bojana Miranović¹, Milena Pandrc², Ljubinko Đenić¹

¹ Klinika za grudnu hirurgiju, Vojnomedicinska akademija, Beograd, Srbija
² Odeljenje stacionarnog lečenja Vojne akademije, Beograd, Srbija

 

• The paper was received on 10.11.2015. / Accepted on 14.12.2015.

 

Abstract

 

Introduction. Kartagener ’s syndrome is a hereditary autosome-recesive disease which is characterized by the structual and general imotile cilia of spermatozoids, bronchial epitel and situs inversus (1) .The main aim of this artical is to point out the importance of the surgical treatment in the prevention of the complications of the Kartagener ’s syndrome.
Case report. A male patient, in the age of  37 with Kartagener ’s syndrome and  thorax anomaly – pectus carinatum  is diagnosed by multislice computerized tomography
(MSCT) , that emphased  an inversion of thoracal and abdominal organs. The spermogram is pointed out the  imotile spermatozoids beacuse of a ciliary dyskinesia, but not infertility which is very frequent in this syndrome(2) . The disorders in ventilation of the obstructive-restrictive type and of the arterial gase were presented. The left posterior lobectomy and a lower lobectomy were done.
Conclusion. Elective surgical treatment of the Kartagener’s syndrome decreases a repetition of respiratory infections.

 

 

References

 

1. Plavec Goran, Tomić Ilija, Škaro-Milić Anđelija B., Radojčić Branko, Aćimović SlobodanPlavec G. Primarna cilijarna diskinezija.
   Vojnosanitetski pregled
   2004, vol. 61, br. 1, str. 89-94, doi:10.2298/VSP0401089P;
2. J.P.Bent III, A.K.Badhey, E.B.Willis. Kartagener’s syndrome, Monteifore. Medscape, 2002;
3. Ciliary dyskinesia, primary; 1, CKD 1; Online Mendelin Inheritance in Man (OMIN), 2013.
4. Skeik N, Jabr Fi; Karatgener’s syndrome. Int J Gen Med. 2011 Jan 12; 4:41-3.doi 10.2147/IJGM. S16181
5. Knott L. Kartagener’s syndrome. Online Patient 23.04.2014.
6. Primary ciliary dyskinesia (2013). American Lung Association. Retrived May 19, 2013 from http:// www.lung.org/lung-dissease/primary ciliary - dyskinesia
7. Krucik G. Kartagener’ s syndrome, 2013. Medically Reviewed on 05.06.2013. from http:// www.healthline.com/health/ Kartagener’s syndrome
8. Michel L,  Lantin F and  Vandeperre J. Surgical treatment of bronchiectasis in Kartagener’s syndrome.British Journal of Surgery. 2005 Dec; 63:494-496.doi:10.1002/bjs.1800630624.

PDF Marić N. • MD-Medical Data 2015;7(4): 319-321